Ross_syndrome

Ross' syndrome

Ross' syndrome

Symptoms of Adie syndrome plus segmental anhidrosis

Ross' syndrome consists of Adie's syndrome (myotonic pupils and absent deep tendon reflexes) plus segmental anhidrosis (typically associated with compensatory hyperhidrosis).[1]

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It was characterized in 1958[2][3] by A.T. Ross.[4]

By 1992, eighteen cases had been documented.[5]

Signs and Symptoms

Initial manifestations often include an abnormal segmental sweating response (described as hyperhidrosis or anhidrosis in some patients) and a tonic pupil. Other commonly reported symptoms included fatigue, chronic cough, and increased urinary frequency.[6]

Prognosis

Ross syndrome is a non life-threatening benign condition but delay in diagnosis can result in slow progression of autonomic symptoms. [7]

Epidemiology

Ross Syndrome is a progressive autonomic dysfunction that can occur in any age, ethnicity, or gender. The average age of diagnosis for Ross syndrome is 36 years and affects more females than males.[7]

See also

References

  1. [1]
    Bolognia JL, Jorizzo JL, Rapini RP, eds. (2007). Dermatology: 2-Volume Set (2nd ed.). St. Louis: Mosby. p. 539. ISBN 978-1-4160-2999-1.
  2. [2]
    Otto Braun-Falco (2000). Dermatology. Springer. pp. 1093–. ISBN 978-3-540-59452-9. Retrieved 20 November 2010.
  3. [3]
    Yaşar S, Aslan C, Serdar ZA, Demirci GT, Tutkavul K, Babalik D (April 2010). "Ross syndrome: Unilateral hyperhidrosis, Adie's tonic pupils and diffuse areflexia". J Dtsch Dermatol Ges. 8 (12): 1004–1006. doi:10.1111/j.1610-0387.2010.07400.x. PMID 20408939. S2CID 24213039.
  4. [4]
    Ross AT (November 1958). "Progressive selective sudomotor denervation; a case with coexisting Adie's syndrome". Neurology. 8 (11): 809–17. doi:10.1212/wnl.8.11.809. PMID 13590391. S2CID 2610900.
  5. [5]
    Weller M, Wilhelm H, Sommer N, Dichgans J, Wiethölter H (April 1992). "Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature". J. Neurol. 239 (4): 231–4. doi:10.1007/BF00839146. PMID 1597691. S2CID 8832477.
  6. [6]
    Lamotte, Guillaume; Sandroni, Paola; Cutsforth-Gregory, Jeremy K.; Berini, Sarah E.; Benarroch, Eduardo E.; Shouman, Kamal; Mauermann, Michelle L.; Anderson, Jennifer; Low, Phillip A.; Singer, Wolfgang; Coon, Elizabeth A. (2021-10-01). "Clinical presentation and autonomic profile in Ross syndrome". Journal of Neurology. 268 (10): 3852–3860. doi:10.1007/s00415-021-10531-8. ISSN 1432-1459. PMC 9639164. PMID 33813643.
  7. [7]
    "Ross syndrome | DermNet NZ". dermnetnz.org. Retrieved 2021-12-07.
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