Ivemark_Syndrome
Asplenia with cardiovascular anomalies
Medical condition
Asplenia with cardiovascular anomalies, also known as Ivemark syndrome and right atrial isomerism,[1] is an example of a heterotaxy syndrome. These uncommon congenital disorders are characterized by defects in the heart, spleen and paired organs such as the lungs and kidneys. Another name is "asplenia-cardiovascular defect-heterotaxy".[2]
Right atrial isomerism is named for its discoverer, Swedish pathologist Biörn Ivemark.[3]